Loading...
Dernières publications
-
Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
-
Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
-
Ingo Riederer, Daniella Arêas Mendes-Da-Cruz, Guilherme Cordenonsi da Fonseca, Mariela Natacha González, Otavio Brustolini, et al.. Zika virus disrupts gene expression in human myoblasts and myotubes: Relationship with susceptibility to infection. PLoS Neglected Tropical Diseases, 2022, 16 (2), pp.e0010166. ⟨10.1371/journal.pntd.0010166⟩. ⟨hal-03832616⟩
Chiffres clés
98
Publications avec texte intégral
Open Access
59 %
Mots clés
Actin
Myoblasts
Nuclear envelope
Triplet expansion disease
Alphavirus
Thérapie génique
Anti-fibrotic pharmacotherapies
Anti-acetylcholine receptor antibodies
Annexin A2
Muscle stem cells
DMD
Neuromuscular junction NMJ
FAPs
Atrophy
PABPN1
Antiserum
AUTOPHAGY
Cross-bridge kinetics
Muscle
APOPTOSIS
Accelerometry
Biomarker
CD49d
Skeletal muscle
Ageing
Aggregate
Myositis
Lamins
Myopathy
Arbovirus
Exon-skipping
C2 domains
Bile salt hydrolases
AChR antibodies
FSHD
Alzheimer's disease
PABPN1 agregates
Cell therapy
Bioinformatics
Dystrophin
CNOT6L
Gene therapy
RNA
Satellite cell
Bioinformatique
Dystrophie musculaire oculopharyngée
Myosin
DUX4
Sarcopenia
AAV vectors
Muscle fibrosis
DNA methylation
Antisens oligonucleotides
Satellite cells
C2C12 cells
Gene replacement
Adipose tissue
MUTATIONS
Muscle strength
Human
ARN
Myopathies
Geriatric assessment
Aav-U7
Inflammation
Aged
Oculopharyngeal muscular dystrophy
Dysferlin
Xenograft
Biopsies humaines
Autologous
Botulinum neurotoxin
Calcium
Myogenesis
Fibrosis
Andermann syndrome
GENE
Muscle dystrophy
Myoblast
BINDING SPECIFICITY
Haploinsufficiency
Pharyngeal muscle
Metabolism
AAV
Myotube
Duchenne muscular dystrophy
Autoimmune diseases
Akt
2-D PAGE
Dysferlinopathy
Regeneration
OPMD
ALS
Functional genomics
Differentiation
Transcriptomics
Intercellular communication
CS
Pax7
Agrégats de PABPN1