Pharmacological inhibition of carnitine palmitoyltransferase 1 restores mitochondrial oxidative phosphorylation in human trifunctional protein deficient fibroblasts

Bruno Lefort (1) , Elodie Gouache (1) , Cécile Acquaviva (2) , Marine Tardieu (1) , Jean François Benoist , Jean-François Dumas (1) , Stéphane Servais (1) , Stephan Chevalier (1) , Christine Vianey-Saban (3) , François Labarthe (1)

1 N2Cox - Niche, Nutrition, Cancer et métabolisme oxydatif
2 Service de Maladies Héréditaires du Métabolisme
3 CarMeN - Cardiovasculaire, métabolisme, diabétologie et nutrition

Domaines: Cancer; Alimentation et Nutrition

Bruno Lefort, Elodie Gouache, Cécile Acquaviva, Marine Tardieu, Jean François Benoist, et al.. Pharmacological inhibition of carnitine palmitoyltransferase 1 restores mitochondrial oxidative phosphorylation in human trifunctional protein deficient fibroblasts. Biochimica et Biophysica Acta - Molecular Basis of Disease, 2017, 1863 (6), pp.1292-1299. ⟨10.1016/j.bbadis.2017.04.005⟩. ⟨hal-02954623⟩