Transport and distribution of 3-hydroxyglutaric acid before and during induced encephalopathic crises in a mouse model of glutaric aciduria type 1

Britta Keyser (1) , Markus Glatzel (2) , Franziska Stellmer (1) , Bastian Kortmann (1) , Zoltan Lukacs (1) , Stefan Kölker (3) , Sven W. Sauer (3) , Nicole Muschol (1) , Wilhelm Herdering (4) , Joachim Thiem (4) , Stephen I. Goodman (5) , David M. Koeller (6) , Kurt Ullrich (1) , Thomas Braulke (1) , Chris Mühlhausen (1)

1 Department of Biochemistry
2 Department of Neuropathology
3 Division of Inherited Metabolic Diseases
4 University of Hamburg
5 Department of Pediatrics
6 Department of Pediatrics [Bearverton]

Mots clés: Life Sciences

Britta Keyser, Markus Glatzel, Franziska Stellmer, Bastian Kortmann, Zoltan Lukacs, et al.. Transport and distribution of 3-hydroxyglutaric acid before and during induced encephalopathic crises in a mouse model of glutaric aciduria type 1. Biochimica et Biophysica Acta - Molecular Basis of Disease, 2008, 1782 (6), pp.385. ⟨10.1016/j.bbadis.2008.02.008⟩. ⟨hal-00501571⟩